肺泡软组织肉瘤
Alveolar soft part sarcoma.
作者信息
Singh Aarti, Gupta Sunita, Ghosh Sujoy, Yuwanati Monal Bhaurao
机构信息
Department of Oral Medicine and Radiology, Maulana Azad Institute of Dental Sciences, New Delhi, India.
出版信息
BMJ Case Rep. 2014 Apr 10;2014:bcr2013203386. doi: 10.1136/bcr-2013-203386.
Alveolar soft part sarcoma (ASPS) is a rare form of soft tissue sarcoma and is most often seen in adolescents and young adults. Despite its unique histology and well-characterised genetic translocation, many questions remain regarding the pathogenesis and treatment of this tumour type. Surgical excision of the primary tumour and pulmonary metastases has resulted in prolonged survival of some patients while the benefit of adjuvant chemotherapy and/or radiotherapy has been disputed. A 35-year-old woman presented with a tumour in the right leg and right side of the mandible along with active metastasis to lungs and multiple skeletal sites.
肺泡软组织肉瘤（ASPS）是一种罕见的软组织肉瘤形式，最常见于青少年和年轻成年人。尽管其具有独特的组织学特征和明确的基因易位，但关于这种肿瘤类型的发病机制和治疗仍存在许多问题。对原发性肿瘤和肺转移灶进行手术切除已使一些患者的生存期延长，而辅助化疗和/或放疗的益处一直存在争议。一名35岁女性患者出现右腿和下颌骨右侧肿瘤，并伴有肺和多个骨骼部位的活跃转移。
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