Min Daniel, Lee Ji-Hyun, Jeong Hye-Cheol, Kim Jung-Hyun, Shin Suk-Pyo, Kim Hong-Min, Han Kyu Hyun, Jeong Hye Yun, Kim Eun-Kyung
Department of Internal Medicine, Bundang CHA Medical Center, CHA University College of Medicine, Seongnam, Korea.
Tuberc Respir Dis (Seoul). 2014 Mar;76(3):136-40. doi: 10.4046/trd.2014.76.3.136. Epub 2014 Mar 29.
Pulmonary artery sarcoma (PAS) is a rare, poorly differentiated malignancy arising from the intimal layer of the pulmonary artery. Contrast-enhanced chest computed tomography (CT) is a good diagnostic modality that shows a low-attenuation filling defect of the pulmonary artery in PAS patients. An 18-year-old man was referred to our hospital for the evaluation and management of cavitary pulmonary lesions that did not respond to treatment. A contrast-enhanced CT of the chest was performed, which showed a filling defect within the right interlobar pulmonary artery. The patient underwent a curative right pneumonectomy after confirmation of PAS. Although lung parenchymal lesions of PAS are generally nonspecific, it can be presented as cavities indicate pulmonary infarcts. Clinicians must consider the possibility of PAS as well as pulmonary thromboembolism in patients with pulmonary infarcts. So, we report the case with PAS that was diagnosed during the evaluation of cavitary pulmonary lesions and reviewed the literatures.
肺动脉肉瘤（PAS）是一种罕见的、起源于肺动脉内膜层的低分化恶性肿瘤。对比增强胸部计算机断层扫描（CT）是一种很好的诊断方法，在PAS患者中可显示肺动脉的低密度充盈缺损。一名18岁男性因治疗无效的空洞性肺部病变被转诊至我院进行评估和治疗。进行了胸部对比增强CT检查，结果显示右肺叶间动脉内有充盈缺损。在确诊为PAS后，患者接受了根治性右肺切除术。虽然PAS的肺实质病变通常不具有特异性，但它可表现为空洞，提示肺梗死。临床医生在患有肺梗死的患者中必须考虑PAS以及肺血栓栓塞的可能性。因此，我们报告了在评估空洞性肺部病变期间诊断为PAS的病例，并复习了相关文献。
