Diagnostic Haemostasis, Haematology Department, Institute of Clinical Pathology and Medical Research (ICPMR), Pathology West, Westmead Hospital, Westmead, NSW, Australia.
Haemophilia. 2014 May;20 Suppl 4:59-64. doi: 10.1111/hae.12414.
The diagnosis and management of bleeding disorders is made difficult by the complexity and variety of disorders, clinical symptoms and bleeding type and severity. von Willebrand disease (VWD) and platelet disorders are disorders of primary haemostasis and together represent the most common inherited bleeding disorders. In this article, we describe the diagnosis of VWD and platelet disorders and the treatment options for VWD.
由于出血性疾病的复杂性和多样性、临床表现以及出血类型和严重程度的不同,出血性疾病的诊断和管理颇具难度。血管性血友病(von Willebrand disease,VWD)和血小板疾病是原发性止血障碍,它们共同代表了最常见的遗传性出血性疾病。本文将描述 VWD 和血小板疾病的诊断方法,以及 VWD 的治疗选择。