Arifin Muhammad Z, Yudoyono Farid, Dahlan Rully H, Hernowo Bethy S, Sutiono Agung B, Faried Ahmad
Department of Neurosurgery, Universitas Padjadjaran-Dr. Hasan Sadikin General Hospital, Bandung, Indonesia ; Department of Oncology Working Group, Health Research Unit, Universitas Padjadjaran-Dr. Hasan Sadikin General Hospital, Bandung, Indonesia.
Department of Neurosurgery, Universitas Padjadjaran-Dr. Hasan Sadikin General Hospital, Bandung, Indonesia.
Surg Neurol Int. 2014 Apr 1;5:45. doi: 10.4103/2152-7806.129909. eCollection 2014.
Giant dermatofibrosarcoma protuberans (DFSP) of the scalp is a rare case, which is an intermediate grade soft tissue neoplasm originating from the dermal layer of the skin, which usually occurs in adults.
We describe such a case in a 26-year-old male. A wide local excision of the tumor with a generous tissue margin was performed; microscopic and immunohistochemical findings established the diagnosis of recurrent DFSP.
Our case is unique in that it is presented as a dermatofibrosarcoma protuberans of the scalp, which is an extremely rare clinical entity, and the patient remains well after 14 months with no further treatment, without any tumor recurrence.
头皮巨大隆突性皮肤纤维肉瘤（DFSP）是一种罕见病例，它是起源于皮肤真皮层的中间级软组织肿瘤，通常发生于成年人。
我们描述了一名26岁男性的此类病例。对肿瘤进行了广泛的局部切除，切缘组织充分；显微镜检查和免疫组化结果确诊为复发性DFSP。
我们的病例独特之处在于它表现为头皮隆突性皮肤纤维肉瘤，这是一种极其罕见的临床实体，患者在未接受进一步治疗的情况下，14个月后情况良好，无肿瘤复发。
