Graf M, Zaczkiewicz M, Torzewski J, Zimmermann O
Cardiovascular Center Oberallgäu-Kempten, Sana Kliniken AG, Clinic Immenstadt, 87509 Immenstadt, Germany.
Case Rep Cardiol. 2012;2012:126764. doi: 10.1155/2012/126764. Epub 2012 Nov 24.
Background. The congenitally corrected transposition of the great arteries (L-TGA) is a very rare congenital heart defect, which often remains undetected for several decades of life. Case Presentation. We report on a 45-year-old man without prior history of heart disease, presenting with cardiac shock related to a first episode of tachycardic atrial fibrillation. The diagnostic work-up identified a L-TGA as the underlying cause for acute heart failure. Discussion. L-TGA is a very rare congenital heart defect, which is characterized by an atrioventricular as well as a ventriculoarterial discordance. By this means, the physiological sequence of pulmonary and systemic circulation is still maintained. On the basis of an ongoing strain of the right ventricle, which has to carry the burden of the systemic blood pressure, after more than four decades without symptoms, acute heart failure was triggered by a tachycardic atrial fibrillation.
背景。先天性矫正型大动脉转位（L-TGA）是一种非常罕见的先天性心脏缺陷，通常在数十年的生命中未被发现。病例报告。我们报告一名45岁男性，既往无心脏病史，因首次发作的快速性心房颤动出现心源性休克。诊断检查确定L-TGA为急性心力衰竭的潜在病因。讨论。L-TGA是一种非常罕见的先天性心脏缺陷，其特征是房室以及心室动脉不一致。通过这种方式，肺循环和体循环的生理顺序仍得以维持。由于右心室持续承受体循环血压的负担，在无症状超过四十多年后，快速性心房颤动引发了急性心力衰竭。
