Ghorbnazadeh Atefeh, Zirak Nahid, Fazlinezhad Afsoon, Moenipour Aliasghar, Manshadi Hamid Hoseinikhah, Teshnizi Mohammad Abbasi
Medical Student, Student Research Committee, Mashhad University of Medical Science, Mashhad, Iran.
M.D., Associate Professor, Department of Anesthesiology, Faculty of Medicine, Imam Reza Hospital, Mashhad University of Medical Science, Mashhad, Iran.
Electron Physician. 2017 Jan 25;9(1):3570-3574. doi: 10.19082/3570. eCollection 2017 Jan.
Situs inversus with levocardia and congenitally corrected transposition of the great arteries represents a relatively very rare congenital condition and most patients are diagnosed in infancy or early age. This case report describes a 35-year old man with congenitally corrected transposition of the great arteries which presented with a five month history of exertional dyspnea. A diagnosis was confirmed by transesophageal echocardiogram, showing situs inversus, levocardia, atrioventricular and ventriculoarterial discordance. He underwent physiologic repair, and was discharged thirty five days after the operation, in a good general condition. Although management of the corrected transposition of the great arteries patients remains controversial, the recommendation is that physiologic repair may be the procedure of choice for some patients, particularly complicated cases.
镜像右位心伴左位心及先天性矫正型大动脉转位是一种相对非常罕见的先天性疾病,大多数患者在婴儿期或幼年时被诊断出来。本病例报告描述了一名35岁男性,患有先天性矫正型大动脉转位,出现劳力性呼吸困难5个月病史。经食管超声心动图确诊,显示镜像右位心、左位心、房室和心室动脉不一致。他接受了生理性修复手术,术后35天出院,全身状况良好。尽管先天性矫正型大动脉转位患者的治疗仍存在争议,但建议生理性修复可能是某些患者,尤其是复杂病例的首选手术方式。