Ouali Sana, Kacem Slim, Gribaa Rim, Neffeti Elyes, Remedi Fahmi, Boughzela Essia
La Rabta Hospital, Tunis, Tunisia.
Sahloul Hospital, Sousse, Tunisia.
Egypt Heart J. 2017 Sep;69(3):219-222. doi: 10.1016/j.ehj.2017.05.002. Epub 2017 May 26.
Congenitally corrected transposition of the great arteries is a rare heart defect that can be associated with systemic ventricular dysfunction and conduction disturbances. The use of cardiac resynchronization therapy in patients with congenital heart disease is not fully established, and achievement of successful pregnancies after implantation of transvenous, biventricular system has never been described, and which resulted in a significant clinical improvement. We describe a 33-year-old female with congenitally corrected transposition of the great arteries, who achieved six pregnancies and successful vaginal deliveries. The two last pregnancies were achieved after cardiac resynchronization therapy for systemic ventricular dysfunction and complete heart block. A congenital cardiac disease has been identified in only one offspring.
先天性矫正型大动脉转位是一种罕见的心脏缺陷，可能与体循环心室功能障碍和传导紊乱有关。先天性心脏病患者使用心脏再同步治疗尚未完全确立，经静脉植入双心室系统后成功妊娠并取得显著临床改善的情况从未有过报道。我们描述了一名33岁患有先天性矫正型大动脉转位的女性，她成功妊娠6次并经阴道顺利分娩。最后两次妊娠是在因体循环心室功能障碍和完全性心脏传导阻滞接受心脏再同步治疗后实现的。仅在一名后代中发现了先天性心脏病。
