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A zebrafish model exemplifies the long preclinical period of motor neuron disease.

作者信息

Ramesh Tennore M, Shaw Pamela J, McDearmid Jonathan

机构信息

Department of Neuroscience, Sheffield Institute for Translational Neuroscience, University of Sheffield, Sheffield, UK.

Department of Biology, University of Leicester, Leicester, UK.

出版信息

J Neurol Neurosurg Psychiatry. 2014 Nov;85(11):1288-9. doi: 10.1136/jnnp-2014-308288. Epub 2014 Jun 26.

DOI:10.1136/jnnp-2014-308288
PMID:24970908
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4215267/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b29d/4215267/7e4445dd534b/jnnp-2014-308288f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b29d/4215267/7e4445dd534b/jnnp-2014-308288f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b29d/4215267/7e4445dd534b/jnnp-2014-308288f01.jpg

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本文引用的文献

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J Neurol Neurosurg Psychiatry. 2014 Nov;85(11):1232-8. doi: 10.1136/jnnp-2013-307135. Epub 2014 Mar 19.
2
Early interneuron dysfunction in ALS: insights from a mutant sod1 zebrafish model.肌萎缩侧索硬化症中的早期中间神经元功能障碍:来自突变 sod1 斑马鱼模型的见解。
Ann Neurol. 2013 Feb;73(2):246-58. doi: 10.1002/ana.23780. Epub 2012 Dec 31.
3
A genetic model of amyotrophic lateral sclerosis in zebrafish displays phenotypic hallmarks of motoneuron disease.
经颅磁刺激在研究肌萎缩侧索硬化症上运动神经元功能障碍中的应用
Brain Sci. 2021 Jul 9;11(7):906. doi: 10.3390/brainsci11070906.
4
The interaction of genetics and environmental toxicants in amyotrophic lateral sclerosis: results from animal models.肌萎缩侧索硬化症中基因与环境毒物的相互作用:来自动物模型的结果
Neural Regen Res. 2017 Jun;12(6):902-905. doi: 10.4103/1673-5374.208564.
5
ZNStress: a high-throughput drug screening protocol for identification of compounds modulating neuronal stress in the transgenic mutant sod1G93R zebrafish model of amyotrophic lateral sclerosis.锌应激:一种用于在肌萎缩侧索硬化症转基因突变体sod1G93R斑马鱼模型中鉴定调节神经元应激化合物的高通量药物筛选方案。
Mol Neurodegener. 2016 Jul 26;11(1):56. doi: 10.1186/s13024-016-0122-3.
6
Preferential PPAR-α activation reduces neuroinflammation, and blocks neurodegeneration in vivo.PPAR-α的选择性激活可减轻神经炎症,并在体内阻止神经退行性变。
Hum Mol Genet. 2016 Jan 15;25(2):317-27. doi: 10.1093/hmg/ddv477. Epub 2015 Nov 24.
7
Cortical Function in Asymptomatic Carriers and Patients With C9orf72 Amyotrophic Lateral Sclerosis.C9orf72 型肌萎缩侧索硬化症无症状携带者和患者的皮质功能
JAMA Neurol. 2015 Nov;72(11):1268-74. doi: 10.1001/jamaneurol.2015.1872.
斑马鱼中的肌萎缩侧索硬化症遗传模型显示运动神经元疾病的表型特征。
Dis Model Mech. 2010 Sep-Oct;3(9-10):652-62. doi: 10.1242/dmm.005538. Epub 2010 May 26.
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High threshold for induction of the stress response in motor neurons is associated with failure to activate HSF1.运动神经元中应激反应诱导的高阈值与未能激活热休克因子1相关。
J Neurosci. 2003 Jul 2;23(13):5789-98. doi: 10.1523/JNEUROSCI.23-13-05789.2003.