罕见类型的膀胱癌：恶性纤维组织细胞瘤。

Rare type of bladder cancer: malign fibrous histiocytoma.

作者信息

Celik Orcun, Turk Hakan, Budak Salih, Ilbey Yusuf Ozlem

机构信息

Tepecik Educational and Research Hospital, Urology Clinic, Izmir.

出版信息

Arch Ital Urol Androl. 2014 Jun 30;86(2):158-9. doi: 10.4081/aiua.2014.2.158.

DOI:10.4081/aiua.2014.2.158

PMID:25017607

Abstract

Malignant fibrous histocytoma (MFH) is the most common soft tissue sarcoma in adults. Urinary tract is a very rare location for MFH. Involvement of the bladder is more common in males and at the 6th decade of life. A case of MFH of the bladder with poor prognosis is presented. Prognostic factors for MFH are tumor grade, amount of invasion, age, tumor size, and histological type. Survival rate is very low and 3-year disease specific survival is approximately 40%.

摘要

恶性纤维组织细胞瘤（MFH）是成人中最常见的软组织肉瘤。泌尿道是MFH非常罕见的发病部位。膀胱受累在男性中更常见，发病年龄多在60岁左右。本文报告一例预后较差的膀胱MFH病例。MFH的预后因素包括肿瘤分级、浸润程度、年龄、肿瘤大小和组织学类型。生存率非常低，3年疾病特异性生存率约为40%。