Fu S J, Weng N Q
Zhonghua Yan Ke Za Zhi. 1989 Jan;25(1):15-7.
Retinal detachment associated with congenital coloboma of choroid is an unusual type of the disease 32 cases (34 eyes), or 1.23% of all 2,602 cases of retinal detachment, were operated on during 1980 to 1986. 17 (53%) patients were under 20 years of age and 28(88%) under 30 years. Preoperative visual acuities ranged from light perception to 0.2, and 25 eyes(74%) under 0.05. The associated congenital abnormalities were coloboma of iris in 32 eyes(94%), cataract in 25(74%), microcornea in 17(50%), and nystagmus in 13(38%). The detection of breaks in the rudimentary retina was extremely difficult, with a positive rate of only 56%, and immediate operative success was obtained in 18 eyes(53%), which were followed up for an average 36 months with re-detachment in 5 eyes. The rate of long term operative success was 38%. With the choroidal coloboma below the optic disc, the retinal breaks outside of the coloboma or in the coloboma near the edge, or the detachment involving at most 3 quadrants of the fundus, the rates of operative success were 81%, 70%, and 100% respectively.
视网膜脱离合并先天性脉络膜缺损是一种不常见的疾病类型。1980年至1986年期间，对32例（34只眼）此类患者进行了手术，占所有2602例视网膜脱离患者的1.23%。17例（53%）患者年龄在20岁以下，28例（88%）在30岁以下。术前视力范围从光感至0.2，25只眼（74%）视力低于0.05。相关的先天性异常包括32只眼（94%）有虹膜缺损、25只眼（74%）有白内障、17只眼（50%）有小角膜、13只眼（38%）有眼球震颤。检测发育不全视网膜的裂孔极其困难，阳性率仅为56%，18只眼（53%）立即获得手术成功，平均随访36个月，5只眼再次发生视网膜脱离。长期手术成功率为38%。对于视盘下方有脉络膜缺损、缺损外或边缘处有视网膜裂孔、或脱离最多累及眼底3个象限的情况，手术成功率分别为81%、70%和1
