Chapman Kristin O, Demetriades Anna M
Department of Ophthalmology, Weill Cornell Medical Center, New York, NY.
J Glaucoma. 2015 Jun-Jul;24(5):e142-4. doi: 10.1097/IJG.0000000000000161.
Iridoschisis is a rare condition in which there is localized cleavage of the iris stroma into 2 layers. It can be associated with plateau iris and more often with either angle closure or open-angle glaucoma. It usually presents in later life as a bilateral progressive condition, however, in this article we present a young adult with bilateral iridoschisis and incomplete plateau iris configuration.
We report the case of a 22-year-old male with bilateral sensorineural hearing loss who presented to clinic for general ophthalmology evaluation. He had no prior ocular history. Examination findings revealed bilateral iridoschisis with incomplete plateau iris configuration. His ocular examination was otherwise unremarkable except for bilateral retinal pigment epithelium mottling. His work-up for glaucoma including optic disc evaluation, visual field testing, and imaging was all within normal limits.
This case is unusual in its presentation of a young patient with bilateral iridoschisis and incomplete plateau iris configuration. Iridoschisis is more commonly a senile process and the presence of iridoschisis in a young adult prompts a review of congenital causes and associations. Although this patient had no evidence of glaucoma at this time, given the associated risk, it is important that he continue to have regular follow-up at this time.
虹膜劈裂症是一种罕见病症,其中虹膜基质局灶性分裂为两层。它可能与高褶虹膜相关,更常见的是与闭角型或开角型青光眼相关。它通常在晚年表现为双侧进行性病症,然而,在本文中,我们介绍了一位患有双侧虹膜劈裂症和不完全高褶虹膜形态的年轻成年人。
我们报告了一例22岁男性双侧感音神经性听力损失患者,他到诊所进行普通眼科评估。他既往无眼部病史。检查结果显示双侧虹膜劈裂症伴不完全高褶虹膜形态。除双侧视网膜色素上皮斑驳外,他的眼部检查其他方面均无异常。他的青光眼检查,包括视盘评估、视野测试和影像学检查均在正常范围内。
该病例的不同寻常之处在于,它表现为一名患有双侧虹膜劈裂症和不完全高褶虹膜形态的年轻患者。虹膜劈裂症更常见于老年过程,年轻成年人出现虹膜劈裂症促使我们对先天性病因及关联因素进行重新审视。尽管该患者目前没有青光眼的证据,但鉴于相关风险,他此时继续定期随访很重要。