Jagadisan Barath, Krishnamurthy Sriram, Raghavan Renitha, Barathi S Deepak
Departments of Pediatrics and *Radiodiagnosis, JIPMER, Pondicherry, India. Correspondence to: Dr Sriram Krishnamurthy, Associate Professor, Department of Pediatrics, JIPMER, Pondicherry 605 006, India.
Indian Pediatr. 2014 Oct;51(10):829-30. doi: 10.1007/s13312-014-0510-0.
Chronic hypoxemia is generally attributed to primary cardiac or pulmonary entities.
A 9-year-old boy presenting with cyanosis, clubbing and hypoxemia, without icterus or hepatosplenomegaly. Cardiovascular and respiratory system examinations were normal.
He was diagnosed as type IB Abernethy malformation, a rare cause of hepatopulmonary syndrome.
Pediatricians should consider hepatopulmonary syndrome in the differential diagnosis of chronic hypoxemia, even in the absence of jaundice or hepatosplenomegaly.
慢性低氧血症通常归因于原发性心脏或肺部疾病。
一名9岁男孩，表现为发绀、杵状指和低氧血症，无黄疸或肝脾肿大。心血管和呼吸系统检查正常。
他被诊断为IB型阿伯内西畸形，这是肝肺综合征的一种罕见病因。
儿科医生在慢性低氧血症的鉴别诊断中应考虑肝肺综合征，即使没有黄疸或肝脾肿大。
