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左心室心肌致密化不全的评估与管理

Evaluation and management of left ventricular noncompaction cardiomyopathy.

作者信息

Stacey R Brandon, Caine Augustus J, Hundley W Gregory

机构信息

Department of Internal Medicine Section on Cardiology, Wake Forest University School of Medicine, Winston-Salem, NC, 27157, USA,

出版信息

Curr Heart Fail Rep. 2015 Feb;12(1):61-7. doi: 10.1007/s11897-014-0237-1.

DOI:10.1007/s11897-014-0237-1
PMID:25399629
Abstract

Left ventricular (LV) noncompaction cardiomyopathy (LVNC) is a form of cardiomyopathy in which trabeculations fail to "compact" with the left ventricular endocardium during fetal cardiac development and is classically associated with subsequent impairment of LV function, significant mortality, ventricular dysrhythmias, and embolic phenomena. As awareness and medical imaging quality have improved, it is becoming easier to identify trabeculations that traverse the LV cavity and serve as a distinguishing feature of this disorder. Differentiating true noncompaction from mild increases in trabeculations requires prudent imaging and clinical correlation. This review seeks to discuss the potential methods of evaluating left ventricular trabeculations, the role of increased trabeculations in cardiovascular disease, and how their presence may affect clinical management.

摘要

左心室(LV)心肌致密化不全心肌病(LVNC)是一种心肌病,在胎儿心脏发育过程中,小梁未能与左心室心内膜“致密化”,通常与随后的左心室功能损害、高死亡率、室性心律失常和栓塞现象相关。随着认识的提高和医学成像质量的改善,识别穿过左心室腔的小梁变得更加容易,这些小梁是这种疾病的一个显著特征。将真正的心肌致密化不全与小梁轻度增加区分开来需要谨慎的成像和临床关联。本综述旨在讨论评估左心室小梁的潜在方法、小梁增加在心血管疾病中的作用以及它们的存在可能如何影响临床管理。

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本文引用的文献

1
Left ventricular noncompaction associated with hypertrophic cardiomyopathy: echocardiographic diagnosis and genetic analysis of a new pedigree in China.左心室心肌致密化不全合并肥厚型心肌病:中国一新家系的超声心动图诊断及遗传学分析。
Int J Cardiol. 2014 Jun 15;174(2):249-59. doi: 10.1016/j.ijcard.2014.03.006. Epub 2014 Mar 15.
2
Clinical spectrum of isolated left ventricular noncompaction: thromboembolic events, malignant left ventricular arrhythmias, and refractory heart failure.孤立性左心室心肌致密化不全的临床谱:血栓栓塞事件、恶性左室心律失常及难治性心力衰竭。
J Am Coll Cardiol. 2014 Apr 29;63(16):e39. doi: 10.1016/j.jacc.2013.11.063. Epub 2014 Mar 5.
3
Circ Res. 2023 Jun 23;133(1):48-67. doi: 10.1161/CIRCRESAHA.122.322223. Epub 2023 May 31.
4
Case Report: Novel Likely Pathogenic Variant Causing Heterogeneous Phenotype in a Korean Family With Left Ventricular Non-compaction.病例报告:韩国一个左心室心肌致密化不全家族中导致异质性表型的新型可能致病变异
Front Pediatr. 2021 Mar 30;9:609389. doi: 10.3389/fped.2021.609389. eCollection 2021.
5
Left Ventricular Noncompaction: New Insights into a Poorly Understood Disease.左心室心肌致密化不全:一种认识不足的疾病的新见解。
Curr Cardiol Rev. 2021;17(2):209-216. doi: 10.2174/1573403X16666200716151015.
6
Use of sacubitril/valsartan in non-compaction cardiomyopathy: a case report.沙库巴曲缬沙坦在非致密化心肌病中的应用:一例报告
ESC Heart Fail. 2020 Jun;7(3):1186-1189. doi: 10.1002/ehf2.12713. Epub 2020 Apr 17.
7
Intact Imaging of Human Heart Structure Using X-ray Phase-Contrast Tomography.使用X射线相衬断层扫描对人体心脏结构进行完整成像。
Pediatr Cardiol. 2017 Feb;38(2):390-393. doi: 10.1007/s00246-016-1527-z. Epub 2016 Nov 30.
Left ventricular noncompaction in patients with bicuspid aortic valve.
二叶式主动脉瓣患者的左心室心肌致密化不全。
J Am Soc Echocardiogr. 2013 Nov;26(11):1306-13. doi: 10.1016/j.echo.2013.08.003. Epub 2013 Sep 14.
4
Comparison of systolic and diastolic criteria for isolated LV noncompaction in CMR.比较 MRI 中孤立性左心室肥厚伴舒张功能不全的收缩和舒张标准。
JACC Cardiovasc Imaging. 2013 Sep;6(9):931-40. doi: 10.1016/j.jcmg.2013.01.014. Epub 2013 Jun 13.
5
2013 ACCF/AHA guideline for the management of heart failure: a report of the American College of Cardiology Foundation/American Heart Association Task Force on Practice Guidelines.2013年美国心脏病学会基金会/美国心脏协会实践指南工作组关于心力衰竭管理的指南:美国心脏病学会基金会/美国心脏协会报告
J Am Coll Cardiol. 2013 Oct 15;62(16):e147-239. doi: 10.1016/j.jacc.2013.05.019. Epub 2013 Jun 5.
6
Mortality and sudden death in pediatric left ventricular noncompaction in a tertiary referral center.三级转诊中心小儿左室心肌致密化不全的死亡率和猝死。
Circulation. 2013 Jun 4;127(22):2202-8. doi: 10.1161/CIRCULATIONAHA.113.002511. Epub 2013 Apr 30.
7
Left ventricular noncompaction (LVNC) and low mitochondrial membrane potential are specific for Barth syndrome.左心室致密化不全(LVNC)和低线粒体膜电位是巴德-希利综合征的特异性表现。
J Inherit Metab Dis. 2013 Nov;36(6):929-37. doi: 10.1007/s10545-013-9584-4. Epub 2013 Jan 30.
8
Multiple left ventricular thrombi in a patient with left ventricular noncompaction.左心室心肌致密化不全患者出现多个左心室血栓。
Tex Heart Inst J. 2012;39(4):550-3.
9
Frequency of asymptomatic disease among family members with noncompaction cardiomyopathy.非致密性心肌病患者家庭成员无症状疾病的频率。
Am J Cardiol. 2012 Nov 15;110(10):1512-7. doi: 10.1016/j.amjcard.2012.07.009. Epub 2012 Aug 8.
10
Isolated left ventricular noncompaction with a congenital aneurysm presenting with recurrent embolism.孤立性左心室心肌致密化不全合并先天性动脉瘤伴反复栓塞。
J Cardiovasc Ultrasound. 2012 Jun;20(2):103-7. doi: 10.4250/jcu.2012.20.2.103. Epub 2012 Jun 25.