Moon Byung Hoo, Park Sang Kyu, Han Young-Min
Department of Neurosurgery, Incheon St. Mary's Hospital, The Catholic University of Korea College of Medicine, Incheon, Korea.
Brain Tumor Res Treat. 2014 Oct;2(2):128-31. doi: 10.14791/btrt.2014.2.2.128. Epub 2014 Oct 31.
Hemangioblastomas (HBMs) in the cerebellopontine angle (CPA) have rarely been reported. When they are within the CPA, they may be misdiagnosed as vestibular schwannoma (VS) or cystic meningioma. Therefore, differential diagnosis is important for the safe treatment of the lesion. Large solid HBMs, similar to intracranial arteriovenous malformations (AVMs), are difficult to surgically remove from an eloquent area because of their location and hypervascularity. We report a case of an HBM in the CPA, which manifested as a hearing impairment or VS. Similar to AVM surgery, the tumor was widely opened and removed en bloc without a new neurological complication using the modified transcondylar fossa approach without resection of the jugular tubercle. Accurate diagnosis, pre-operative embolization, and a tailored approach were essential for the safe treatment of the HBM in the CPA.
小脑脑桥角（CPA）的血管母细胞瘤（HBM）鲜有报道。当它们位于CPA内时，可能会被误诊为前庭神经鞘瘤（VS）或囊性脑膜瘤。因此，鉴别诊断对于该病变的安全治疗至关重要。大型实性HBM与颅内动静脉畸形（AVM）相似，由于其位置和高血管性，很难从功能区手术切除。我们报告一例CPA内的HBM，其表现为听力障碍或VS。与AVM手术类似，采用改良经髁窝入路，未切除颈静脉结节，将肿瘤广泛打开并整块切除，未出现新的神经并发症。准确的诊断、术前栓塞和个体化的手术方法对于CPA内HBM的安全治疗至关重要。
