Kord Valeshabad Ali, Xiao Lekui, Amin-Hanjani Sepideh, Alsadi Alaa, Valyi-Nagy Tibor, Kim Jinsuh
Department of Radiology, University of Illinois at Chicago, Chicago, Illinois, United States.
Department of Neurosurgery, University of Illinois at Chicago, Chicago, Illinois, United States.
J Neurol Surg Rep. 2018 Oct;79(4):e98-e102. doi: 10.1055/s-0038-1676455. Epub 2018 Dec 12.
To describe an extremely rare case of sporadic hemangioblastoma (HB) within the cavernous sinus and Meckel's cave with extension to the cerebellopontine angle (CPA) cistern. A 73-year-old male presented with hearing loss, unilateral ptosis, and facial numbness. The imaging showed a complex cystic-solid mass centered at the left cavernous sinus and Meckel's cave with extension to the CPA cistern. Patient underwent retrosigmoid craniectomy for partial resection of the CPA angle component of the mass. Surgical pathology confirmed the diagnosis of HB and patient was scheduled for subsequent radiotherapy of the residual mass. We present an exceptional case of supratentorial HB without associated von Hippel-Lindau (VHL) disease, which was predominantly located in the cavernous sinus and Meckel's cave and led to multiple cranial nerve symptoms. We describe imaging characteristics and radiologic-pathologic correlation of this atypically located HB, which can be difficult to consider in the differential diagnosis presurgically.
描述一例极为罕见的散发性血管母细胞瘤（HB），位于海绵窦和梅克尔腔，并延伸至桥小脑角（CPA）池。一名73岁男性，出现听力丧失、单侧眼睑下垂和面部麻木。影像学检查显示，一个复杂的囊实性肿块，以左侧海绵窦和梅克尔腔为中心，并延伸至CPA池。患者接受了乙状窦后开颅手术，以部分切除肿块的CPA角部分。手术病理证实为HB，患者计划对残余肿块进行后续放疗。我们报告了一例幕上HB的特殊病例，无相关的冯·希佩尔-林道（VHL）病，主要位于海绵窦和梅克尔腔，并导致多种颅神经症状。我们描述了这种非典型位置HB的影像学特征及放射学-病理学相关性，术前鉴别诊断时很难考虑到这种情况。
