网状血管内皮瘤：一种罕见的儿童血管性肿瘤。

Retiform hemangioendothelioma: an uncommon pediatric vascular neoplasm.

作者信息

Ranga Swaroop M, Kuchangi Nischal C, Shankar Vijay S, Amita K, Haleuoor Basavaraj B, Belagola Sathyanarayana D

机构信息

Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Bangalore, Karnataka, India.

Department of Pathology, Adichunchanagiri Institute of Medical Sciences, Bangalore, Karnataka, India.

出版信息

Indian J Dermatol. 2014 Nov;59(6):633. doi: 10.4103/0019-5154.143583.

DOI:10.4103/0019-5154.143583

PMID:25484427

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4248535/

Abstract

Retiform hemangioendothelioma is considered as a low grade angiosarcoma, commonly seen in 2(nd)-4(th) decade of life. The youngest patient reported is of 9 years of age. A 9-year-old boy was presented with an asymptomatic red patch on the chest since 1 year. There was an erythematous patch with nodule of about 5 mm near the distal margin. Biopsy from the nodule revealed numerous thin-walled branching vessels in dermis resembling rete testis, suggestive of retiform hemangioendothelioma. We, hereby, report this case for its rarity and uncommon clinical presentation in childhood period.

摘要

网状血管内皮瘤被认为是一种低级别血管肉瘤，常见于20至40岁人群。有报道的最年轻患者为9岁。一名9岁男孩自1年前起胸部出现无症状红色斑块。在远端边缘附近有一个约5毫米的红斑结节。对该结节进行活检发现真皮内有许多薄壁分支血管，类似睾丸网，提示为网状血管内皮瘤。我们特此报告该病例，因其在儿童期罕见且临床表现不常见。