O'Duffy F, Timon C, Toner M
Department of Otorhinolaryngology, Royal Victoria Eye and Ear Hospital, Dublin, Ireland.
J Laryngol Otol. 2012 Feb;126(2):200-2. doi: 10.1017/S0022215111002398. Epub 2011 Sep 5.
We report the case of a rare angiosarcoma, retiform haemangioendothelioma, in an 18-year-old young man, which presented as a recurrent ulcerating lesion of the left pinna.
Case report and literature review of retiform haemangioendothelioma. This is a low grade angiosarcoma with a high local recurrence rate and low metastasis rate, and was first described in 1994 by Calonje et al.
This patient represents only the third report of lymph node metastasis in a case of retiform haemangioendothelioma. To date, 31 cases of the tumour have been reported. Histological diagnosis of this group of vascular neoplasms can be challenging, as their histopathological appearance is intermediate between haemangioma and angiosarcoma.
Surgical excision remains the primary treatment modality, with adjuvant radiotherapy recommended in patients with large tumour size, local recurrence and lymph node metastasis, as seen in this case.
我们报告一例18岁青年男性罕见的血管肉瘤——网状血管内皮瘤病例，该病例表现为左耳反复出现的溃疡性病变。
网状血管内皮瘤的病例报告及文献综述。这是一种低级别血管肉瘤，局部复发率高，转移率低，1994年由卡洛尼等人首次描述。
该患者是网状血管内皮瘤发生淋巴结转移的第三例报告。迄今为止，已报告31例该肿瘤病例。这组血管肿瘤的组织学诊断具有挑战性，因为其组织病理学表现介于血管瘤和血管肉瘤之间。
手术切除仍然是主要的治疗方式，对于肿瘤体积大、局部复发和淋巴结转移的患者，如本病例所见，建议辅助放疗。
