多发性网状血管内皮瘤。一种低级别血管肉瘤。

Multiple retiform hemangioendotheliomas. A low-grade angiosarcoma.

作者信息

Duke D, Dvorak A, Harris T J, Cohen L M

机构信息

Harvard Medical School, Boston, MA, USA.

出版信息

Am J Dermatopathol. 1996 Dec;18(6):606-10. doi: 10.1097/00000372-199612000-00010.

DOI:10.1097/00000372-199612000-00010

PMID:8989934

Abstract

We present the case of a 30-year-old woman who over a 10-year period has developed multiple well-differentiated angiosarcomas involving the trunk and extremities. The clinical and histologic features are characteristic of retiform hemangioendothelioma (RH), a distinctive form of low-grade angiosarcoma. This case is unique in that multiple lesions developed in different anatomic sites. We discuss the clinical and histologic characteristics, diagnosis, and prognosis of RH.

摘要

我们报告了一例30岁女性的病例，该患者在10年时间里发生了多处分化良好的血管肉瘤，累及躯干和四肢。临床和组织学特征符合网状血管内皮瘤（RH），这是一种独特的低级别血管肉瘤形式。该病例的独特之处在于不同解剖部位出现了多个病变。我们讨论了RH的临床和组织学特征、诊断及预后。