1例罕见的胸段脊髓脊膜膨出合并1型脊髓纵裂畸形，伴低位脊髓栓系、背侧脊髓空洞症和骶骨发育不全：五联征表现。

A rare case of thoracic myelocystocele associated with type 1 split cord malformation with low lying tethered cord, dorsal syrinx and sacral agenesis: Pentad finding.

作者信息

Mankotia Dipanker Singh, Satyarthee Guru Dutta, Sharma Bhawani Shankar

机构信息

Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India.

出版信息

J Neurosci Rural Pract. 2015 Jan;6(1):87-90. doi: 10.4103/0976-3147.143209.

DOI:10.4103/0976-3147.143209

PMID:25552859

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4244798/

Abstract

Myelocystocele is a rare form of spinal dysraphism. Thoracic myelocystocele is still rarer. The occurrence of thoracic myelocystocele associated with type-1 split cord malformation, low lying tethered cord, dorsal syrinx and spina bifida is extremely rare. Clinical presentation of such a rare case and an early surgical management is discussed briefly.

摘要

脊髓脊膜膨出是一种罕见的脊柱裂形式。胸段脊髓脊膜膨出更为罕见。胸段脊髓脊膜膨出合并1型脊髓纵裂畸形、低位脊髓栓系、脊髓空洞症和脊柱裂的情况极为罕见。本文简要讨论了这一罕见病例的临床表现及早期手术治疗。