Nishinarita Reiko, Mihara Takahiro, Nakamura Nobuhito, Miyamoto Yoshihisa, Ka Koui
Department of Anesthesiology, Kanagawa Children's Medical Center, Mutsukawa 2-138-4, Minami-ku, Yokohama, Japan.
J Anesth. 2015 Jun;29(3):450-452. doi: 10.1007/s00540-014-1955-y. Epub 2015 Jan 21.
Emanuel syndrome is a rare anomaly associated with multiple systemic malformations. We present two cases involving pediatric patients with Emanuel syndrome. The first patient presented with micrognathia and had patent ductus arteriosus and a single kidney. The patient was difficult to intubate with McGRATH(®) but was successfully intubated with an Airtraq(®) device. The second patient did not present with micrognathia and was not difficult to intubate. A thorough examination of the heart, kidney, and spinal cord is important when planning the anesthetic management of patients with Emanuel syndrome. Moreover, adequate preparation for a difficult airway is essential, and the Airtraq(®) device may be useful for intubating patients with Emanuel syndrome with micrognathia.
伊曼纽尔综合征是一种与多种全身畸形相关的罕见异常。我们报告两例涉及患有伊曼纽尔综合征的儿科患者的病例。首例患者表现为小颌畸形,患有动脉导管未闭和单肾。使用麦格拉思(®)喉镜为该患者插管困难,但使用艾特瑞(®)设备成功插管。第二例患者未表现出小颌畸形,插管也不困难。在规划伊曼纽尔综合征患者的麻醉管理时,对心脏、肾脏和脊髓进行全面检查很重要。此外,为困难气道做好充分准备至关重要,艾特瑞(®)设备可能有助于为患有小颌畸形的伊曼纽尔综合征患者插管。