儿童孤立性左心室心肌致密化不全：两例不同表现病例
Isolated left ventricular noncompaction in children: two cases with different manifestations.
作者信息
Karacan Mehmet, Olgun Hasim, Yildirim Zuhal Keskin, Ceviz Naci
机构信息
Atatürk University, Faculty of Medicine, Department of Pediatrics, Division of Pediatric Cardiology, Erzurum, Turkey.
Atatürk University, Faculty of Medicine, Department of Pediatrics, Erzurum, Turkey.
出版信息
Eurasian J Med. 2008 Dec;40(3):144-7.
Abstract
Isolated noncompaction of the ventricular myocardium is an uncommon disorder characterized by an excessively prominent trabecular meshwork seen in the early period of embryogenesis. The clinical presentation of noncompaction includes a high prevalence of heart failure, thromboembolic events and arrhythmias. Echocardiography is the procedure of choice for the diagnosis of noncompaction. We report two demonstrative patients with isolated noncompaction of the left ventricular myocardium and review the available related literature.
摘要
孤立性心室心肌致密化不全是一种罕见的疾病，其特征是在胚胎发育早期出现过度突出的小梁网状结构。致密化不全的临床表现包括心力衰竭、血栓栓塞事件和心律失常的高发生率。超声心动图是诊断致密化不全的首选检查方法。我们报告了两例左心室心肌孤立性致密化不全的典型病例，并回顾了现有的相关文献。
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引用本文的文献
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