Kumar Ajay, Lodha Rakesh, Kumar Prawin, Kabra S K
Departments of Pediatrics, Vardhaman Mahavir Medical College and Safdarjang Hospital, New Delhi; and *All India Institute of Medical Sciences, New Delhi, India. Correspondence to: Dr SK Kabra, Professor, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi, India.
Indian Pediatr. 2015 Jan;52(1):35-7. doi: 10.1007/s13312-015-0563-8.
To describe clinical profile, etiology and outcome in children with non-cystic fibrosis bronchiectasis.
A chart review of children diagnosed with non-cystic fibrosis bronchiectasis, attending pediatric chest clinic of tertiary care hospital.
The underlying cause was identified in 51 (63.8%) out of 80 children (mean age, 9.6 y). Common causes were post-infectious in 19 (23.8%), suspected primary ciliary dyskinesia in 12 (15%), and allergic bronchopulmonary aspergillosis in 6 (7.5%). One or more complications were observed in 76 (95%) patients; 14 (17.5%) children required surgery and 5 (11.1%) children died.
Common causes of non-cystic fibrosis bronchiectasis are post infectious and primary ciliary dyskinesia. There is a need to create awareness about early diagnosis of bronchiectasis as it is often delayed.
描述非囊性纤维化支气管扩张症患儿的临床特征、病因及预后。
对在三级医院儿科胸科门诊就诊的诊断为非囊性纤维化支气管扩张症的患儿进行病历回顾。
80名患儿（平均年龄9.6岁）中，51名（63.8%）明确了潜在病因。常见病因包括感染后19例（23.8%）、疑似原发性纤毛运动障碍12例（15%）、变应性支气管肺曲霉病6例（7.5%）。76例（95%）患者出现一种或多种并发症；14例（17.5%）患儿需要手术，5例（11.1%）患儿死亡。
非囊性纤维化支气管扩张症的常见病因是感染后及原发性纤毛运动障碍。由于支气管扩张症的诊断常常延迟，有必要提高对其早期诊断的认识。
