Toomarian Lida, Mashhadiabbas Fatemeh, Mirkarimi Mahkameh, Mehrdad Leili
Pediatric Department, Zahedan University of Medical Sciences, Zahedan, Iran.
J Med Case Rep. 2010 Jan 7;4:1. doi: 10.1186/1752-1947-4-1.
Dentin dysplasia is a rare hereditary disturbance of dentin formation characterized by defective dentin development with clinically normal appearing crowns, severe hypermobility of teeth and spontaneous dental abscesses or cysts. Radiographic analysis shows obliteration of all pulp chambers, short, blunted and malformed or absent roots and peri-apical radiolucencies of non carious teeth.
We present a case of dentin dysplasia type I in a 12-year-old Iranian boy, and the clinical, radiographic and histopathologic findings of this condition and treatment are described.
There are still many inconclusive issues in the diagnosis and management of patients with dentin dysplasia. The diagnostic features of this rare disturbance will remain incompletely defined until additional cases have been described. Early diagnosis of the condition and initiation of effective regular dental treatments may help these patients to prevent or delay loss of dentition.
牙本质发育异常是一种罕见的牙本质形成遗传性紊乱疾病，其特征为牙本质发育缺陷，临床表现为牙冠外观正常、牙齿严重松动以及自发性牙脓肿或囊肿。影像学分析显示所有牙髓腔闭塞、牙根短粗、畸形或缺失，以及非龋性牙齿的根尖周透射区。
我们报告了一名12岁伊朗男孩的I型牙本质发育异常病例，并描述了该疾病的临床、影像学和组织病理学表现及治疗情况。
牙本质发育异常患者的诊断和管理仍存在许多不确定的问题。在描述更多病例之前，这种罕见紊乱疾病的诊断特征仍将不完全明确。早期诊断并开始有效的定期牙科治疗可能有助于这些患者预防或延缓牙列缺失。
