Yi Xiaoping, Xiao Desheng, Long Xueying
Department of Radiology, Xiangya Hospital, Central South University Changsha 410008, China.
Department of Pathology, Xiangya Hospital, Central South University Changsha 410008, China.
Int J Clin Exp Pathol. 2015 Jan 1;8(1):1073-6. eCollection 2015.
We recently encountered a giant Myofibroblastic sarcoma (MS) exceeding 23 cm in diameter which had developed in the liver in a 27-year-old female, and which was surgically resected with gratifying results. On surveillance imaging, a giant mass was detected in the right lobe of the liver. One the basis of morphology and immunohistochemistry features, the diagnosis of intermediate-grade myofibroblastic sarcoma (MS) was established. MS is extremely rarely found in the abdominal cavity. It is almost impossible to make a definite diagnosis before operation. However, the possibility of sarcoma should be taken into account for liver mass according to multimodal imaging features of the mass, especially when the diagnosis of common hepatic tumor was not supported by signs on imaging. Relative characteristic features on multimodal images maybe helpful to considerate the possibility of MS. This is the first reported case to date.
我们最近遇到一例直径超过23厘米的巨大肌成纤维细胞肉瘤(MS),该肿瘤发生在一名27岁女性的肝脏中,并通过手术切除,效果良好。在监测成像中,肝脏右叶发现一个巨大肿块。根据形态学和免疫组化特征,确诊为中级肌成纤维细胞肉瘤(MS)。MS在腹腔中极为罕见。术前几乎不可能做出明确诊断。然而,根据肿块的多模态影像学特征,对于肝脏肿块应考虑肉瘤的可能性,特别是当影像学表现不支持常见肝脏肿瘤的诊断时。多模态图像上的相对特征性表现可能有助于考虑MS的可能性。这是迄今为止首例报道的病例。