Kumar Rajan, Das Kuntal Kanti, Jaiswal Awadhesh Kumar, Mehrotra Anant, Sahu Rabi Narayan, Srivastava Arun Kumar, Jaiswal Sushila, Behari Sanjay
Department of Neurosurgery, SGPGIMS, Lucknow, Uttar Pradesh, India.
Department of Pathology, SGPGIMS, Lucknow, Uttar Pradesh, India.
Asian J Neurosurg. 2015 Jan-Mar;10(1):53. doi: 10.4103/1793-5482.151520.
An 11-year-old boy presented with holocranial headache associated with vomiting and heaviness in right paranasal region. On examination, he had left sided upper motor neuron type facial palsy along with a subtle ipsilateral hemiparesis (grade 4/5 Medical Research Council). Magnetic resonance imaging brain revealed a contrast enhancing large well-defined extra-axial mass lesion in right middle cranial fossa with extension into the infratemporal fossa. The mass was excised in two stages. Histopathology was suggestive of clear cell meningioma (CCM). Supratentorial pediatric CCM is a rare entity. The case is discussed along with review of literature on this rare clinico-pathological entity.
一名11岁男孩出现全颅头痛,伴有呕吐及右侧鼻旁区域沉重感。检查发现,他有左侧上运动神经元型面瘫,同时伴有轻微的同侧偏瘫(医学研究委员会肌力分级为4/5级)。脑部磁共振成像显示,右侧中颅窝有一个边界清晰、强化明显的大型轴外肿块病变,并延伸至颞下窝。该肿块分两期切除。组织病理学提示为透明细胞脑膜瘤(CCM)。幕上儿童CCM是一种罕见的疾病。本文结合对该罕见临床病理实体的文献回顾对该病例进行了讨论。