Celebi Filiz, Pilanci Kezban Nur, Saglam Sezer, Balci Numan Cem
Department of Radiology, Gayrettepe Florence Nightingale Hospital, Istanbul 34340, Turkey.
Department of Oncology, Istanbul Bilim University, Istanbul 34340, Turkey.
Oncol Lett. 2015 Apr;9(4):1937-1939. doi: 10.3892/ol.2015.2902. Epub 2015 Jan 27.
Angiosarcoma is an extremely rare, high-grade malignancy, which accounts for <2% of all soft-tissue sarcomas. Cases of primary renal angiosarcoma represent 1% of these. Angiosarcomas involving the kidney usually originate from metastatic skin lesions or primary visceral lesions and most often occur in the sixth and seventh decades of life. The present study describes a case of primary renal angiosarcoma that presented as a large right-sided renal mass with symptoms of flank pain. Despite surgical removal of the tumor, recurrent disease with associated lung metastases was identified at the surgical site following adjuvant chemotherapy. The patient succumbed to the disease 13 months after the diagnosis.
血管肉瘤是一种极其罕见的高级别恶性肿瘤，占所有软组织肉瘤的比例不到2%。原发性肾血管肉瘤病例占其中的1%。累及肾脏的血管肉瘤通常起源于转移性皮肤病变或原发性内脏病变，最常发生在60和70岁年龄段。本研究描述了一例原发性肾血管肉瘤病例，该病例表现为右侧肾脏巨大肿块并伴有胁腹疼痛症状。尽管手术切除了肿瘤，但辅助化疗后在手术部位发现了伴有肺转移的复发性疾病。患者在诊断后13个月死于该疾病。
