Darlington Danny, Anitha Fatima Shirly
Urology, Government Stanley Medical College and Hospital, Chennai, IND.
Pediatrics, Church of South India Kalyani Multispeciality Hospital, Chennai, IND.
Cureus. 2019 Jan 7;11(1):e3841. doi: 10.7759/cureus.3841.
Primary renal angiosarcoma is an exceedingly rare malignancy of the kidney. It usually presents in the elderly with metastatic disease and dismal prognosis. Treatment protocols are not standardized for this very rare renal malignancy. We report the case of a young man who was incidentally diagnosed with primary renal angiosarcoma. Preoperative imaging was suggestive of renal cell carcinoma; however, postoperative histopathological examination confirmed it to be an angiosarcoma. The patient was treated with surgical excision followed by adjuvant chemotherapy and is doing well at one-year follow-up.
原发性肾血管肉瘤是一种极其罕见的肾脏恶性肿瘤。它通常在老年患者中出现，伴有转移性疾病，预后不佳。对于这种非常罕见的肾脏恶性肿瘤，治疗方案尚未标准化。我们报告了一例偶然诊断为原发性肾血管肉瘤的年轻男性病例。术前影像学检查提示为肾细胞癌；然而，术后组织病理学检查证实为血管肉瘤。该患者接受了手术切除，随后进行辅助化疗，在一年的随访中情况良好。
