完全性背侧胰腺发育不全、盘状肾和双角子宫三联征。一种关联还是偶然发现：文献中的首例病例。
A triad of complete dorsal pancreatic agenesis, pancake kidney and bicornuate uterus. An association or an incidental finding: first case in literature.
作者信息
Lal Anupam, Pavunesan Santhosh Kumar, Mahalingam Harshavardhan, Garg Mandeep, Sinha Saroj K, Khandelwal Niranjan
机构信息
Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research. Chandigarh, India.
出版信息
JOP. 2015 Mar 20;16(2):189-91. doi: 10.6092/1590-8577/2949.
CONTEXT
Agenesis of the dorsal pancreas is a rare congenital anomaly which can be detected either incidentally during imaging or encountered during investigation for pancreas related pathologies such as pancreatitis or diabetes mellitus. Few associations of this condition with heterotaxy syndrome, pancreatic tumors and congenital heart disease have been described.
CASE REPORT
We report a novel association of genitourinary anomalies in a case of complete dorsal pancreatic agenesis not previously described in the literature.
CONCLUSION
Knowledge about dorsal pancreatic agenesis is essential for radiologist in patients presenting with unexplained pain abdomen and its association with various conditions may help radiologist in assisting clinician in management of these patients.
背景
背侧胰腺发育不全是一种罕见的先天性异常，可在影像学检查时偶然发现，或在针对胰腺炎或糖尿病等胰腺相关疾病的检查过程中被发现。这种情况与内脏反位综合征、胰腺肿瘤和先天性心脏病的关联鲜有报道。
病例报告
我们报告了一例完全性背侧胰腺发育不全病例中存在泌尿生殖系统异常的新关联，此前文献中未曾描述过。
结论
对于出现不明原因腹痛的患者，放射科医生了解背侧胰腺发育不全至关重要，其与各种病症的关联可能有助于放射科医生协助临床医生管理这些患者。
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