完全性背侧胰腺发育不全及单侧肾发育不全。

Moreira Adriana, Carvalho André, Portugal Inês, Jesus José Miguel

Department of Radiology, Centro Hospitalar de São João, Alameda Prof. Hêrnani Monteiro, 4200-319 Porto, Portugal.

Radiol Case Rep. 2017 Dec 1;13(1):68-71. doi: 10.1016/j.radcr.2017.10.025. eCollection 2018 Feb.

Dorsal pancreatic agenesis is a very rare congenital anomaly. Unilateral renal agenesis, on the other hand, is a relatively common congenital anomaly, although its etiology is not fully understood. Renal and pancreatic embryologic development appears to be nonrelated. We report a case of a 34-year-old man who was referred to our hospital for evaluation of cholestasis and microalbuminuria. Ultrasound and magnetic resonance imaging examinations showed empty right renal fossa and absence of the pancreatic neck, body, and tail. Our case report is the second case of a dorsal pancreatic agenesis and unilateral renal agenesis in a young male patient.

背侧胰腺发育不全是一种非常罕见的先天性异常。另一方面，单侧肾发育不全是一种相对常见的先天性异常，尽管其病因尚未完全明确。肾脏和胰腺的胚胎发育似乎并无关联。我们报告一例34岁男性患者，因胆汁淤积和微量白蛋白尿前来我院就诊。超声和磁共振成像检查显示右侧肾窝空虚，胰腺颈部、体部和尾部缺如。我们的病例报告是第二例年轻男性患者同时出现背侧胰腺发育不全和单侧肾发育不全的病例。