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一例胰腺背侧发育不全合并单侧肾缺如、单角子宫和卵巢异位：简要综述及学习要点

A case of dorsal agenesis of pancreas associated with unilateral renal agenesis, unicornuate uterus, and ovarian ectopia: A brief review and learning points.

作者信息

Bhandari Arindam, Mandal Samrat

机构信息

Department of Radiology, Kothari Medical Centre, Kolkata, West Bengal, India.

出版信息

Indian J Radiol Imaging. 2020 Jul-Sep;30(3):395-399. doi: 10.4103/ijri.IJRI_165_19. Epub 2020 Oct 15.

DOI:10.4103/ijri.IJRI_165_19
PMID:33273779
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7694721/
Abstract

Dorsal agenesis of the pancreas is a rare entity, with about 100 cases reported. It can be overlooked on ultrasound due to the non visualization of the body and tail of the pancreas. This is due to overlying gas in the stomach, which offers a poor acoustic window and obscures visualization. Renal agenesis and Mullerian duct anomalies are uncommon associations of dorsal agenesis of the pancreas because of the separate embryological origin of the pancreas and genitourinary organs. Here, we present a case of a 17-year-old patient who had dorsal agenesis of the pancreas, associated with unilateral renal agenesis, unicornuate uterus, and ectopic ovary. We describe the anomalies and discuss the radiological differential diagnosis and potential pitfalls. We provide a brief review of the literature with few radiological teaching points and possible genetic implications of the case.

摘要

胰腺背侧发育不全是一种罕见的病症，据报道约有100例。由于胰腺体部和尾部无法显示，超声检查时可能会忽略这种情况。这是因为胃内气体覆盖，提供的声学窗口不佳，从而模糊了视野。由于胰腺和泌尿生殖器官的胚胎起源不同，肾发育不全和苗勒管异常是胰腺背侧发育不全不常见的关联情况。在此，我们报告一例17岁患者，其患有胰腺背侧发育不全，并伴有单侧肾发育不全、单角子宫和异位卵巢。我们描述了这些异常情况，并讨论了放射学鉴别诊断及潜在陷阱。我们对文献进行了简要回顾，提出了一些放射学教学要点以及该病例可能的遗传学意义。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/1166bd09a691/IJRI-30-395-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/b0caf9b7bf6d/IJRI-30-395-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/59f6ae6c3d4f/IJRI-30-395-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/43936b8100d9/IJRI-30-395-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/1e4200157bf3/IJRI-30-395-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/1166bd09a691/IJRI-30-395-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/b0caf9b7bf6d/IJRI-30-395-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/59f6ae6c3d4f/IJRI-30-395-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/43936b8100d9/IJRI-30-395-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/1e4200157bf3/IJRI-30-395-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/183a/7694721/1166bd09a691/IJRI-30-395-g005.jpg

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本文引用的文献

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