Pai Anusha H, George Anne, Adiga Deepa, Girisha Banavasi S
Department of Dermatology, K.S. Hegde Medical Academy, Mangalore, Karnataka, India.
Department of Pathology, Kasturba Medical College, Mangalore, Karnataka, India.
Indian J Dermatol. 2015 Mar-Apr;60(2):215. doi: 10.4103/0019-5154.152602.
Peripheral T cell lymphoma (PTCL) is a heterogeneous group of hematological tumors originating from mature T cells, which constitutes less than 15% of all non-Hodgkins lymphomas in adults. Primary cutaneous PTCL-not otherwise specified (NOS) represent a subgroup of PTCLs with no consistent immunophenotypic, genetic or clinical features. PTCL-NOS frequently has an aggressive course with a tendency for systemic involvement, however, a well-defined therapeutic and prognostic approach has not been outlined yet. We report a case of PTCL-NOS with multiple cutaneous lesions in a young adult male with an emphasis on the treatment modality used.
外周T细胞淋巴瘤(PTCL)是一组异质性血液肿瘤,起源于成熟T细胞,在成人所有非霍奇金淋巴瘤中占比不到15%。原发性皮肤PTCL,未另行特别说明(NOS)是PTCL的一个亚组,没有一致的免疫表型、遗传学或临床特征。PTCL-NOS通常病程侵袭,有全身受累倾向,然而,尚未概述明确的治疗和预后方法。我们报告一例年轻成年男性PTCL-NOS伴多发皮肤损害的病例,并重点介绍所采用的治疗方式。