软骨发育不全与肢体延长：英国队列研究结果及文献综述
Achondroplasia and limb lengthening: Results in a UK cohort and review of the literature.
作者信息
Donaldson James, Aftab Syed, Bradish Christopher
机构信息
Great Ormond Street Hospital for Children, London, UK.
出版信息
J Orthop. 2015 Jan 28;12(1):31-4. doi: 10.1016/j.jor.2015.01.001. eCollection 2015 Mar.
Abstract
AIMS
We aim to review the results, complications and outcomes of a single surgeon's series of lower limb lengthening in patients with achondroplasia.
METHODS
Ten achondroplastic children underwent limb lengthening. The patients, medical records and radiographs were reviewed.
RESULTS
The average age at the time of the index operation was 7.8 years. A single surgeon undertook all procedures. The average total length gain was 20.5 cm. The commonest complication was a fractured femur after removal of the frame.
CONCLUSION
Although complication rates were high (70%), none were left with any long-term sequelae and all were pleased with the results.
摘要
目的
我们旨在回顾一位外科医生对软骨发育不全患者进行的一系列下肢延长手术的结果、并发症及结局。
方法
十名软骨发育不全儿童接受了肢体延长手术。对患者、病历及X光片进行了回顾。
结果
初次手术时的平均年龄为7.8岁。所有手术均由同一位外科医生进行。平均总长度增加了20.5厘米。最常见的并发症是拆除固定架后股骨骨折。
结论
尽管并发症发生率较高（70%），但无一例留下任何长期后遗症，且所有人对结果都很满意。
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