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反复咯血揭示休斯-斯托文综合征

Recurrent Haemoptysis Revealing Hughes-Stovin Syndrome.

作者信息

Moussa Nedia, Znegui Tasnim, Snoussi Mouna, Gargouri Rahma, Bahloul Zouhaier, Abid Sourour, Kammoun Samy

机构信息

Pneumology Department, Hedi Chaker Hospital, Sfax, Tunisia.

Internal Medicine Department, Hedi Chaker Hospital, Sfax, Tunisia.

出版信息

Eur J Case Rep Intern Med. 2021 Oct 5;8(10):002810. doi: 10.12890/2021_002810. eCollection 2021.

Abstract

UNLABELLED

Hughes-Stovin syndrome is a very rare condition with no defined diagnostic criteria. We present the case of a 26-year-old man who had haemoptysis revealing Hughes-Stovin syndrome. We will consider the aetiology, therapeutic and evolutionary aspects of this disease.

LEARNING POINTS

Hughes-Stovin syndrome is a very rare disorder of unknown aetiology which can be fatal.It is considered a variant of Behcet's disease.Early diagnosis and treatment improve prognosis.

摘要

未标注

休斯-斯托文综合征是一种非常罕见的疾病,没有明确的诊断标准。我们报告一例26岁男性咯血病例,该病例被诊断为休斯-斯托文综合征。我们将探讨该疾病的病因、治疗及病情演变方面。

学习要点

休斯-斯托文综合征是一种病因不明的非常罕见的疾病,可能致命。它被认为是白塞病的一种变体。早期诊断和治疗可改善预后。

相似文献

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Recurrent Haemoptysis Revealing Hughes-Stovin Syndrome.反复咯血揭示休斯-斯托文综合征
Eur J Case Rep Intern Med. 2021 Oct 5;8(10):002810. doi: 10.12890/2021_002810. eCollection 2021.

本文引用的文献

7
Moderate hemoptysis caused by hughes-stovin syndrome.休斯-斯托文综合征所致的中度咯血。
Clin Pract. 2014 Nov 6;4(3):647. doi: 10.4081/cp.2014.647. eCollection 2014 Oct 30.
8
Hughes-Stovin syndrome.休斯-斯托文综合征。
Orphanet J Rare Dis. 2011 Apr 13;6:15. doi: 10.1186/1750-1172-6-15.

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