Morandi Anna, Ure Benno, Leva Ernesto, Lacher Martin
Department of Pediatric Surgery, Fondazione IRCCS Ca´Granda, Ospedale Maggiore Policlinico, Via Commenda 10, 20122, Milan, Italy,
Pediatr Surg Int. 2015 Jun;31(6):543-50. doi: 10.1007/s00383-015-3700-5. Epub 2015 Apr 4.
Various management strategies for anorectal malformations (ARM) have been proposed. The aim of this study was to assess the current management in centers of excellence in Europe.
An online survey on the pre- and post-operative concepts, surgical techniques, and the management of complications was sent to the representative experts of 28 selected European centers of pediatric surgery with special expertise in the treatment of ARM.
The survey was completed by 25 experts from 14 countries. To assess the level of the rectal pouch in newborns 60% of participants perform a prone cross-table X-ray and 52% ultrasound. If an ostomy is required, 84% create divided Peña stomas. Primary repair in the newborn period is performed in females with rectoperineal (92%), rectovestibular (60%), and no fistula (32%), and in males with rectoperineal (92%), rectourinary (17%) and no fistula (38%). For 68 % of surgeons, the PSARP is the preferred surgical approach for "low" malformations. Laparoscopically assisted pull-throughs are routinely performed by 48% of experts for ARM with bladderneck and 28% for rectoprostatic fistula. 88% perform postoperative dilations.
The management of ARM in Europe is very heterogeneous. High-quality clinical studies are needed to provide scientific evidence for the optimal treatment strategies.
已提出多种肛门直肠畸形(ARM)的管理策略。本研究的目的是评估欧洲卓越中心目前的管理情况。
一项关于术前和术后概念、手术技术及并发症管理的在线调查被发送给28个选定的欧洲小儿外科中心的代表专家,这些中心在ARM治疗方面具有特殊专业知识。
来自14个国家的25名专家完成了该调查。为评估新生儿直肠盲袋的水平,60%的参与者进行俯卧位十字交叉X线检查,52%进行超声检查。如果需要造口,84%创建改良的佩尼亚造口。新生儿期的一期修复在女性直肠会阴型(92%)、直肠前庭型(60%)和无瘘型(32%),以及男性直肠会阴型(92%)、直肠尿道型(17%)和无瘘型(38%)中进行。对于68%的外科医生来说,经会阴肛门直肠成形术(PSARP)是“低位”畸形的首选手术方法。48%的专家常规对伴有膀胱颈的ARM进行腹腔镜辅助拖出术,28%的专家对直肠前列腺瘘进行该手术。88%的医生进行术后扩张。
欧洲ARM的管理非常多样化。需要高质量的临床研究为最佳治疗策略提供科学依据。