This article outlines the clinical features and investigation of cystic fibrosis. The need for a multidisciplinary approach in specialist centres is highlighted. Future developments, particularly heart lung transplantation and research into the underlying genetic and biochemical abnormality, are discussed.
本文概述了囊性纤维化的临床特征及相关检查。强调了在专科中心采用多学科方法的必要性。还讨论了未来的发展，尤其是心肺移植以及对潜在基因和生化异常的研究。
