Kurian Jujju Jacob, Ninan Pradeep Joseph
Department of Paediatric Surgery, Christian Medical College, Vellore, Tamil Nadu, India.
BMJ Case Rep. 2015 Apr 15;2015:bcr2015209771. doi: 10.1136/bcr-2015-209771.
Childhood cystic partially differentiated nephroblastoma (CPDN) is an uncommon renal neoplasm. Bilateral CPDN or CPDN co-existing with a cystic nephroma/Wilms tumour is extremely rare. Treatment of CPDN is by complete surgical excision. Although local recurrences are uncommon, distant metastases have not been described. We present a case of bilateral CPDN that, after complete excision, recurred as bilateral cystic Wilms tumour. To the best of our knowledge, this is the first reported case in the literature where a bilateral CPDN has recurred as bilateral Wilms tumour.
儿童囊性部分分化型肾母细胞瘤(CPDN)是一种罕见的肾脏肿瘤。双侧CPDN或CPDN与囊性肾瘤/肾母细胞瘤并存极为罕见。CPDN的治疗方法是完整手术切除。虽然局部复发不常见,但尚未见远处转移的报道。我们报告一例双侧CPDN病例,在完整切除后复发为双侧囊性肾母细胞瘤。据我们所知,这是文献中首次报道的双侧CPDN复发为双侧肾母细胞瘤的病例。