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滑膜脂肪瘤病:青少年女性膝关节疼痛的罕见原因。

Synovial lipomatosis: A rare cause of knee pain in an adolescent female.

作者信息

Miladore Nicholas, Childs Mary A, Sabesan Vani J

机构信息

Nicholas Miladore, Mary A Childs, Vani J Sabesan, Department of Orthopaedic Surgery, Western Michigan University Homer Stryker M.D. School of Medicine, Kalamazoo, MI 49008, United States.

出版信息

World J Orthop. 2015 Apr 18;6(3):369-73. doi: 10.5312/wjo.v6.i3.369.

DOI:10.5312/wjo.v6.i3.369
PMID:25893181
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4390900/
Abstract

Synovial lipomatosis is a benign proliferative disease of the subsynovial adipose which can lead to a variety of presentations. Cases of synovial lipomatosis in children or adolescents are rare. This case report describes an adolescent patient with a rare bilateral presentation of synovial lipomatosis. She had been treated for years prior to her presentation for juvenile idiopathic arthritis. She presented with chronic bilateral knee pain, swelling, and mechanical symptoms. Bilateral MR imaging demonstrated effusions, hypertrophy of the synovium, and polyp-like projections of tissue with the same signal intensity as fat which is pathognomonic for synovial lipomatosis. Arthroscopic synovectomy and extensive debridement of polyp like fat projections of the right knee was performed. Histopathology was consistent with the synovial lipomatosis diagnosis. Postoperatively, the patient was satisfied with her outcome with improved pain relief and function in her right knee.

摘要

滑膜脂肪瘤病是一种滑膜下脂肪的良性增生性疾病,可导致多种临床表现。儿童或青少年患滑膜脂肪瘤病的病例罕见。本病例报告描述了一名患有罕见双侧滑膜脂肪瘤病的青少年患者。在她因幼年特发性关节炎就诊之前,已经接受了多年治疗。她表现为双侧膝关节慢性疼痛、肿胀和机械性症状。双侧磁共振成像显示有积液、滑膜肥厚以及与脂肪信号强度相同的息肉样组织突起,这是滑膜脂肪瘤病的特征性表现。对右膝进行了关节镜下滑膜切除术及对息肉样脂肪突起进行广泛清创。组织病理学与滑膜脂肪瘤病的诊断相符。术后,患者对其结果感到满意,右膝疼痛缓解,功能改善。

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引用本文的文献

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Bilateral lipoma arborescens -A proliferative case demonstrating progression in an adolescent male.双侧树状脂肪瘤——一例增生性病例,展示了一名青少年男性的病情进展。
J Orthop. 2018 May 7;15(2):736-740. doi: 10.1016/j.jor.2018.05.022. eCollection 2018 Jun.
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Primary lipoma arborescens of the knee.膝关节原发性树枝状脂肪瘤。
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本文引用的文献

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Juvenile rheumatoid arthritis.青少年类风湿性关节炎
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Orthopedics. 2008 Feb;31(2):185. doi: 10.3928/01477447-20080201-05.
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Lipoma arborescens of the knee.膝关节的树枝状脂肪瘤。
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Lipoma arborescens of the knee: report of a case managed by arthroscopic synovectomy.膝关节树状脂肪瘤:1例关节镜下滑膜切除术治疗病例报告
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Lipoma arborescens (diffuse articular lipomatosis).树枝状脂肪瘤(弥漫性关节脂肪瘤病)。
J South Orthop Assoc. 2003 Fall;12(3):163-6.
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Synovial lipomatosis (lipoma arborescens) affecting multiple joints in a patient with congenital short bowel syndrome.患有先天性短肠综合征的患者出现滑膜脂肪过多症(树枝状脂肪瘤)累及多个关节。
J Rheumatol. 2002 May;29(5):1088-92.