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急性渗出性多形性卵黄样黄斑病变1例:随访及超广角光谱域光学相干断层扫描

A case of acute exudative polymorphous vitelliform maculopathy: follow-up and wide-field spectral-domain optical coherence tomography.

作者信息

Massaro Domenico, Pece Alfredo, Pichi Francesco, Yannuzzi Lawrence A, Gilardoni Francesca, Carrai Paola, Bonsignore Francesco, Nucci Paolo

机构信息

San Giuseppe Hospital, University Eye Clinic, Milan - Italy.

出版信息

Eur J Ophthalmol. 2015 Jul 30;25(5):e91-4. doi: 10.5301/ejo.5000616.

DOI:10.5301/ejo.5000616
PMID:25907291
Abstract

PURPOSE

To present a case of an HIV-positive patient with acute exudative polymorphous vitelliform maculopathy (AEPVM) and evaluate the presence of specific spectral-domain optical coherence tomography (SD-OCT) findings.

METHODS

Case report.

RESULTS

We reviewed the AEPVM cases reported in the literature and compared those to our patient to determine if there is a correspondence between the etiology that leads to the onset of AEPVM and clinical and SD-OCT findings.

CONCLUSIONS

Acute exudative polymorphous vitelliform maculopathy is a disease that involves the outer retinal layers with lipofuscin deposits and serous detachment of the neuroepithelium with or without intraretinal cysts. Not much is known about the etiology and pathogenesis, and not many cases have been described. A review of the few clinical cases reported in the literature does not show a specific correspondence between etiology and SD-OCT findings.

摘要

目的

报告1例人类免疫缺陷病毒(HIV)阳性患者发生急性渗出性多形性卵黄样黄斑病变(AEPVM)的病例,并评估其是否存在特定的频域光学相干断层扫描(SD-OCT)表现。

方法

病例报告。

结果

我们回顾了文献中报道的AEPVM病例,并将其与我们的患者进行比较,以确定导致AEPVM发病的病因与临床及SD-OCT表现之间是否存在对应关系。

结论

急性渗出性多形性卵黄样黄斑病变是一种累及视网膜外层、伴有脂褐素沉积以及神经上皮浆液性脱离(伴或不伴有视网膜内囊肿)的疾病。关于其病因和发病机制知之甚少,且报道的病例不多。对文献中报道的少数临床病例进行回顾,未发现病因与SD-OCT表现之间存在特定的对应关系。

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