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一名6岁男孩发生急性双侧浆液性视网膜脱离并自行消退。

Acute bilateral serous retinal detachments with spontaneous resolution in a 6-year-old boy.

作者信息

Van Camp Sophie, Vande Walle Steffi, Casteels Ingele, Jacob Julie, Cassiman Cathérine, Wouters Carine, Schauwvlieghe Pieter-Paul

机构信息

Department of Ophthalmology, University Hospitals Leuven, Belgium.

Department of Pediatrics, University Hospitals Leuven, Belgium.

出版信息

GMS Ophthalmol Cases. 2020 Aug 25;10:Doc37. doi: 10.3205/oc000164. eCollection 2020.

DOI:10.3205/oc000164
PMID:32884891
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7452953/
Abstract

A healthy 6-year-old boy presented with acute bilateral vision loss, multiple serous retinal detachments between the vascular arcades and a thickened choroid. Spontaneous resolution occurred over several weeks. We hypothesize that the clinical constellation in our patient is suggestive of acute exudative polymorphous vitelliform maculopathy (AEPVM) or might be an atypical presentation of Vogt-Koyanagi-Harada (VKH) disease. We propose that it was caused by an autoimmune-mediated activation of inflammatory cells at the level of the choroid, induced by an unknown trigger.

摘要

一名健康的6岁男孩出现急性双侧视力丧失、血管弓之间多发浆液性视网膜脱离以及脉络膜增厚。数周内病情自行缓解。我们推测,该患者的临床症状提示为急性渗出性多形性卵黄样黄斑病变(AEPVM),或者可能是Vogt-小柳-原田(VKH)病的非典型表现。我们认为,这是由未知触发因素诱导的脉络膜水平炎症细胞的自身免疫介导激活所致。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/56cba974a777/OC-10-37-g-004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/3d634fdecea8/OC-10-37-g-001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/0d00c4215be5/OC-10-37-g-002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/359dc8dba2ba/OC-10-37-g-003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/56cba974a777/OC-10-37-g-004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/3d634fdecea8/OC-10-37-g-001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/0d00c4215be5/OC-10-37-g-002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/359dc8dba2ba/OC-10-37-g-003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2714/7452953/56cba974a777/OC-10-37-g-004.jpg

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本文引用的文献

1
Acute exudative polymorphous vitelliform maculopathy: To bolus or not to bolus?急性渗出性多形性卵黄样黄斑病变:是否进行大剂量注射?
Oman J Ophthalmol. 2018 Sep-Dec;11(3):280-283. doi: 10.4103/ojo.OJO_12_2017.
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Acute Exudative Polymorphous Vitelliform Maculopathy Syndrome; natural history and evolution of fundal and OCT images over time.急性渗出性多形性卵黄样黄斑病变综合征;眼底及光学相干断层扫描(OCT)图像随时间的自然病史及演变
BMJ Case Rep. 2018 Mar 20;2018:bcr-2018-224241. doi: 10.1136/bcr-2018-224241.
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Idiopathic Acute Exudative Polymorphous Vitelliform Maculopathy: Clinical Spectrum and Multimodal Imaging Characteristics.
特发性急性渗出性多形性玻璃膜疣:临床谱和多模态成像特征。
Ophthalmology. 2018 Jan;125(1):75-88. doi: 10.1016/j.ophtha.2017.07.020. Epub 2017 Aug 23.
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Multimodal Imaging Features in Acute Exudative Paraneoplastic Polymorphous Vitelliform Maculopathy.急性渗出性副肿瘤性多形性卵黄样黄斑病变的多模态成像特征
Ophthalmic Surg Lasers Imaging Retina. 2016 Dec 1;47(12):1143-1146. doi: 10.3928/23258160-20161130-09.
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Vogt-Koyanagi-Harada disease.伏格特-小柳-原田病
Surv Ophthalmol. 2017 Jan-Feb;62(1):1-25. doi: 10.1016/j.survophthal.2016.05.002. Epub 2016 May 27.
6
A case of acute exudative polymorphous vitelliform maculopathy: follow-up and wide-field spectral-domain optical coherence tomography.急性渗出性多形性卵黄样黄斑病变1例:随访及超广角光谱域光学相干断层扫描
Eur J Ophthalmol. 2015 Jul 30;25(5):e91-4. doi: 10.5301/ejo.5000616.
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Intravitreal dexamethasone implant for acute exudative polymorphous vitelliform maculopathy.玻璃体内注射地塞米松植入物治疗急性渗出性多形性卵黄样黄斑病变。
Eur J Ophthalmol. 2014 Sep-Oct;24(5):803-7. doi: 10.5301/ejo.5000477. Epub 2014 May 1.
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A case of neurosyphilis revealed by acute exudative polymorphous vitelliform maculopathy.一例由急性渗出性多形性卵黄样黄斑病变揭示的神经梅毒病例。
Ophthalmic Surg Lasers Imaging Retina. 2014 Apr 4;45 Online:e29-31. doi: 10.3928/23258160-20140331-06.
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Acute exudative polymorphous vitelliform maculopathy in a patient with Lyme disease.莱姆病患者的急性渗出性多形性卵黄样黄斑病变
Ophthalmic Surg Lasers Imaging Retina. 2013 Sep-Oct;44(5):493-6. doi: 10.3928/23258160-20130909-14.
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