Maloney William James, Raymond George, Hershkowitz David, Rochlen Glenn
N Y State Dent J. 2015 Mar;81(2):38-41.
Hemophilia is an inherited x-linked recessive disorder. It is known popularly as "The Royal Disease," as it has affected many of the royal families of Europe by virtue of Queen Victoria being a carrier for the gene and, subsequently, passing it on to her offspring. They, in turn, married and had children with other royal families of Europe. Hemophilia is certainly not limited to royalty. There are many hemophiliacs living in our communities, and they must receive both proper dental home-care education and dental treatment in order to prevent possibly life-threatening emergency dental episodes. Individuals with hemophilia pose different management issues to the dental professional. The various precautions and modifications that must be taken in order to ensure the safe delivery of dental care to hemophiliac dental patients are discussed.
血友病是一种遗传性X连锁隐性疾病。它被普遍称为“皇家病”，因为维多利亚女王是该基因的携带者，从而使欧洲许多皇室家族都受到了影响，随后她又将该基因传给了她的后代。而这些后代又与欧洲其他皇室家族通婚并生育子女。血友病当然并不局限于皇室成员。我们的社区中有许多血友病患者，为了预防可能危及生命的紧急牙科情况，他们必须接受适当的家庭口腔护理教育和牙科治疗。血友病患者给牙科专业人员带来了不同的管理问题。本文讨论了为确保向血友病牙科患者安全提供牙科护理而必须采取的各种预防措施和调整方法。
