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一名法洛四联症未矫正的成年长期幸存者的心律失常:病例报告及文献综述

Arrhythmias in a long-term adult survivor with uncorrected tetralogy of Fallot: Case report and review of the literature.

作者信息

Hirst Colin S, Jureidini Saadeh, Hauptman Paul J

机构信息

Department of Medicine, Saint Louis University School of Medicine, St. Louis, MO.

Department of Pediatrics, Saint Louis University School of Medicine, St. Louis, MO.

出版信息

J Electrocardiol. 2015 Jul-Aug;48(4):734-8. doi: 10.1016/j.jelectrocard.2015.04.006. Epub 2015 Apr 10.

Abstract

We present a case of a middle-aged adult with uncorrected Tetralogy of Fallot (TOF) with pulmonary atresia who developed symptomatic supraventricular and ventricular arrhythmias. The lack of data regarding management of electrical and other complications in adults with uncorrected TOF is highlighted and emphasizes the need for a registry to better understand the medical management of long-standing adult survivors.

摘要

我们报告一例患有未经矫正的法洛四联症(TOF)合并肺动脉闭锁的中年成人病例,该患者出现了有症状的室上性和室性心律失常。强调了缺乏关于未经矫正的TOF成年患者电生理及其他并发症管理的数据,并突出了建立登记系统以更好地了解长期存活成年患者医疗管理情况的必要性。

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