Dermatofibrosarcoma protuberans of the vulva: a rare tumor presenting during pregnancy in a teenager.

OBJECTIVES

We report a case of a young patient with dermatofibrosarcoma protuberans of the vulva diagnosed during pregnancy. We also provide a review of the literature on this topic.

MATERIALS AND METHODS

This patient's case was reviewed retrospectively. A current literature search was performed and findings were reported.

RESULTS

This rare malignancy was diagnosed during pregnancy in a teenager.

CONCLUSIONS

Dermatofibrosarcoma protuberans of the vulva, a rare vulvar neoplasm mostly associated with older patients and never before reported during pregnancy, should be considered as part of the differential diagnosis for any vulvar mass and cannot be excluded on the basis of the patient's age or pregnancy status.