Loverro Giuseppe, Resta Leonardo, Di Naro Edoardo, Caringella Anna Maria, Mastrolia Salvatore Andrea, Vicino Mario, Tartagni Massimo, Schonauer Luca Maria
Department of Obstetrics and Gynecology, University Hospital Policlinico of Bari and University of Bari "Aldo Moro", School of Medicine, Piazza Giulio Cesare 11, 70124 Bari, Italy.
Department of Pathology, University Hospital Policlinico of Bari and University of Bari "Aldo Moro", Piazza Giulio Cesare 11, 70124 Bari, Italy.
Case Rep Obstet Gynecol. 2015;2015:871821. doi: 10.1155/2015/871821. Epub 2015 Apr 15.
Ewing sarcoma-primitive neuroectodermal tumors (ES/PNETs) constitute a family of neoplasms characterized by a continuum of neuroectodermal differentiations. ES/PNET of the uterus is rare. There are 48 cases of ES/PNET of the uterus published in the literature as far as we know. We describe a case of Ewing sarcoma of the uterus occurring in a 17-year-old woman presenting with a two-month history of pelvic pain. After surgical excision and microscopic, immunohistochemical, and electron microscopy examination, the diagnosis of Ewing sarcoma of the uterus was suggested. This report will discuss the diagnosis and surgical and clinical management of Ewing uterine sarcoma in young women, according to the available literature. In spite of the rarity of ES/PNETs, they should be taken into account in the differential diagnosis of uterine neoplasms in young women.
尤因肉瘤-原始神经外胚层肿瘤（ES/PNETs）是一类以神经外胚层分化连续为特征的肿瘤。子宫ES/PNET罕见。据我们所知，文献中已发表48例子宫ES/PNET病例。我们描述了1例发生于17岁女性的子宫尤因肉瘤，该患者有2个月的盆腔疼痛病史。经过手术切除以及显微镜、免疫组织化学和电子显微镜检查后，提示为子宫尤因肉瘤。本报告将根据现有文献探讨年轻女性子宫尤因肉瘤的诊断、手术及临床处理。尽管ES/PNET罕见，但在年轻女性子宫肿瘤的鉴别诊断中应予以考虑。
