Cherif Yosra, Zantour Baha, Alaya Wafa, Berriche Olfa, Younes Samia, Sfar Mohamed Habib
Department of Endocrinology and Internal Medicine, Tahar Sfar University Hospital of Mahdia, Hiboun District, 5100 Mahdia, Tunisia.
Case Rep Endocrinol. 2015;2015:735868. doi: 10.1155/2015/735868. Epub 2015 Jun 15.
Various endocrine manifestations are commonly described in myotonic dystrophy (MD), including primary hypogonadism, diabetes mellitus, and thyroid and parathyroid dysfunction. We describe a 46-year-old woman with a family history of MD with her son. She was diagnosed with cardiac arrhythmia and required the implantation of a pacemaker. She was noted to have a bilateral cataract. She complained of muscle weakness, diffuse myalgia, and palpitation. The electromyography (EMG) showed myotonic discharges. Laboratory tests showed high serum calcium 2.83 mmol/L, serum phosphate 1.2 mmol/L, parathormone 362.5 pg/mL, thyroid stimulating hormone TSH 0.02 mIU/L (normal range: 0.34-5.6 mIU/L), FT4 21.17 ng/mL, and negative anti-thyroperoxidase antibodies. Cervical ultrasound revealed a multinodular goiter. The 99mTc-MIBI scintigraphy localized a lower right parathyroid adenoma. The clinical data, the family history of MD, EMG data, and endocrine disturbances were strongly suggestive of MD associated with hyperthyroidism and primary hyperparathyroidism.
强直性肌营养不良(MD)常伴有多种内分泌表现,包括原发性性腺功能减退、糖尿病以及甲状腺和甲状旁腺功能障碍。我们描述了一位46岁女性,她和儿子均有MD家族史。她被诊断为心律失常,需要植入起搏器。她被发现患有双侧白内障。她主诉肌肉无力、弥漫性肌痛和心悸。肌电图(EMG)显示有强直性放电。实验室检查显示血清钙2.83 mmol/L升高,血清磷1.2 mmol/L,甲状旁腺激素362.5 pg/mL,促甲状腺激素TSH 0.02 mIU/L(正常范围:0.34 - 5.6 mIU/L),游离甲状腺素FT4 21.17 ng/mL,抗甲状腺过氧化物酶抗体阴性。颈部超声显示为结节性甲状腺肿。99mTc - MIBI闪烁扫描定位出右下甲状旁腺腺瘤。临床资料、MD家族史、EMG数据以及内分泌紊乱强烈提示MD合并甲状腺功能亢进和原发性甲状旁腺功能亢进。