伴有乳糜胸的全身性淋巴管瘤病
Generalised lymphangiomatosis with chylothorax.
作者信息
Dunkelman H, Sharief N, Berman L, Ninan T
机构信息
Northwick Park Hospital, Harrow.
出版信息
Arch Dis Child. 1989 Jul;64(7):1058-60. doi: 10.1136/adc.64.7.1058.
Abstract
A 9 month old boy presented with acute respiratory distress and was found to have a left pleural effusion. The chylous nature of the effusion, multiple bony lytic lesions, and splenic cysts lead to the diagnosis of congenital lymphangiomatosis with chylothorax. Surgical intervention including pleurectomy was required after unsuccessful conservative management.
摘要
一名9个月大的男童因急性呼吸窘迫就诊，检查发现左侧胸腔积液。积液呈乳糜性、多发骨质溶解病变及脾囊肿，最终诊断为先天性淋巴管瘤病合并乳糜胸。保守治疗失败后，需要进行包括胸膜切除术在内的手术干预。
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