Preda G E, Pasetti P, Caggiula S
Dent Cadmos. 1989 Oct 31;57(16):104-7.
The interest we see in oral pathology about Beckwith-Wiedemann syndrome is not strictly related to the association with neoplasms of the syndrome but, first of all, to the high frequency of macroglossia in the patients affected. In fact this pathologic situation, setting up since birth, can strongly modify the growth of teeth and facial skeleton. Therapy consists in a partial glossectomy. After this reducing is advised a contention applied to the chin.
我们在口腔病理学中看到的对贝克威思-维德曼综合征的兴趣,并非严格与该综合征与肿瘤的关联有关,而是首先与受影响患者中巨舌症的高发生率有关。事实上,这种自出生就存在的病理状况会强烈改变牙齿和面部骨骼的生长。治疗方法包括部分舌切除术。在这种缩减术后,建议对下巴进行固定。