Yildiz Baris D
Ankara Numune Teaching Hospital General Surgery Clinic, Sihhiye, Ankara, Turkey.
Int Surg. 2015 Jun;100(6):1018-20. doi: 10.9738/INTSURG-D-14-00128.1.
Extra-adrenal myelolipomas are rare, benign tumors composed of adipose tissue and hematopoietic cells. Almost all myelolipomas occur within the adrenal gland. Only 50 cases of myelolipomas were described in literature and none of these were associated with gastric mesenchymal neoplasia. A 72-year-old male patient presented to a family medicine outpatient clinic with dyspnea and urinary urgency. His abdominal sonography revealed a 9-cm intra-abdominal mass. An incidental finding was 2 separate masses 1 cm each on the serosal surface of the stomach. The pathology specimen of the retroperitoneal mass revealed myelolipoma histopathology while gastric masses were reported as spindle cell mesenchymal neoplasias. The association of gastric spindle cell tumor and myelolipoma was not reported before in medical literature. Extra-adrenal myelolipomas are rare lesions, but should be considered in the differential diagnosis of fat containing retroperitoneal masses that are well circumscribed.
肾上腺外髓脂肪瘤是一种罕见的由脂肪组织和造血细胞组成的良性肿瘤。几乎所有的髓脂肪瘤都发生在肾上腺内。文献中仅描述了50例髓脂肪瘤,且均与胃间质瘤无关。一名72岁男性患者因呼吸困难和尿急就诊于家庭医学门诊。他的腹部超声检查发现一个9厘米的腹腔内肿块。偶然发现胃浆膜表面有两个分别为1厘米的独立肿块。腹膜后肿块的病理标本显示为髓脂肪瘤组织病理学,而胃肿块报告为梭形细胞间质瘤。胃梭形细胞瘤与髓脂肪瘤的关联在医学文献中此前未见报道。肾上腺外髓脂肪瘤是罕见病变,但在鉴别诊断边界清晰的含脂肪腹膜后肿块时应予以考虑。