Adult Form of Scimitar Syndrome Presenting as Severe Pulmonary Hypertension in a Child.
作者信息
Kalpana Sivasambo, Balaji B Sarath, Elilarasi Selladurai, Solomon Neville A G
机构信息
Department of Pulmonology, Institute of Child Health and Hospital for Children; and *Department of Pediatric Cardiac Surgery, Apollo Childrens Hospital; Chennai, India. Correspondence to: Dr Sivasambo Kalpana, Department of Pulmonology, Institute of Child Health and Hospital for Children, Halls road, Egmore, Chennai.
出版信息
Indian Pediatr. 2015 Oct;52(10):889-90. doi: 10.1007/s13312-015-0738-3.
BACKGROUND
Scimitar syndrome is a rare association of congenital cardiopulmonary anomalies; the adult form is not usually is associated with pulmonary hypertension.
CASE CHARACTERISTICS
6-year-old girl with recurrent episodes of cough and breathlessness, along with features of right heart enlargement. Computed tomography angiogram revealed right pulmonary veins draining into inferior vena cava with dextroposition of heart.
OUTCOME
Successfully managed with surgical correction.
MESSAGE
Scimitar syndrome should be considered in any child with unexplained pulmonary hypertension and dextroposed heart.
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