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膀胱副神经节瘤表现为早发型子痫前期,术后围产期结局良好:一例病例报告及文献复习

Paraganglioma of Urinary Bladder Presenting as An Early Preeclampsia with Successful Perinatal Outcome After Surgery: A Case Report and Review of Literature.

作者信息

Dattatrya Kaje Yogesh, Vedpalsingh Tanwar Harshawardhan, Ravikant Shelke Umesh, Gajendra Singh Abhishek, Kiran Patwardhan Sujata

机构信息

Registrar, Department of Urology, Seth G.S. Medical College and KEM Hospital , Mumbai, Maharashtra, India .

Ex-Registrar, Department of Urology, Seth G.S. Medical College and KEM Hospital , Mumbai, Maharashtra, India .

出版信息

J Clin Diagn Res. 2015 Sep;9(9):PD01-2. doi: 10.7860/JCDR/2015/14306.6420. Epub 2015 Sep 1.

Abstract

Paraganglioma in urinary bladder associated with pregnancy is extremely rare with a prevalence of less than 1%. We report a case of 25-year-old pregnant female who presented with gross haematuria and clot retention during first trimester. MRI pelvis showed a mass antero- inferior to bladder. Transurethral resection biopsy revealed paraganglioma of the urinary bladder. Her workup showed neither raised plasma free normetanephrine levels. Patient underwent partial cystectomy during second trimester. Postoperatively, she is normotensive with normal serum free normetanephrine levels. At term, she delivered a healthy female child. This case highlights a successful perinatal outcome with timely intervention, adequate preoperative control of hypertension and counselling. We report a case of paraganglioma of urinary bladder presenting as an early preeclampsia with successful perinatal outcome after surgery.

摘要

膀胱副神经节瘤合并妊娠极为罕见,患病率低于1%。我们报告一例25岁的妊娠女性,在孕早期出现肉眼血尿和血块潴留。盆腔磁共振成像显示膀胱前下方有一肿块。经尿道切除活检显示为膀胱副神经节瘤。她的检查显示血浆游离去甲变肾上腺素水平均未升高。患者在孕中期接受了部分膀胱切除术。术后,她血压正常,血清游离去甲变肾上腺素水平正常。足月时,她产下一名健康女婴。该病例强调了通过及时干预、充分的术前高血压控制和咨询,可获得成功的围产期结局。我们报告一例膀胱副神经节瘤表现为早发型子痫前期,术后围产期结局成功的病例。

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