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结节病累及心脏:一种预后极差的罕见关联,两例报告

Sarcoidosis with heart involvement: a rare association of terrible prognosis, a report of two cases.

作者信息

Kefi Asma, Ben Abdelhafidh Nadia, Sayhi Sameh, Abid Rim, Ajili Faida, Laabidi Janet, Othmani Salah

机构信息

Department of Internal Medicine, Military Hospital of Tunis, 1008 Montfleury, Tunisia.

出版信息

Pan Afr Med J. 2015 Aug 5;21:243. doi: 10.11604/pamj.2015.21.243.6124. eCollection 2015.

DOI:10.11604/pamj.2015.21.243.6124
PMID:26523183
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4607964/
Abstract

Sarcoidosis is a multisystemic disorder of unknown etiology which is characterized by the formation of non-caseating granulomas in involved tissues. Cardiac involvement is one of the least common manifestations and it can occur at any point of time during the course of sarcoidosis. Here we present the case of 2 patients with known sarcoidosis who develop cardiac abnormalities in the absence of known primary cardiac cause. In our report, we would like to draw attention to the importance of considering heart involvement in any case with systemic sarcoidosis especially in young age.

摘要

结节病是一种病因不明的多系统疾病,其特征是受累组织中形成非干酪样肉芽肿。心脏受累是最不常见的表现之一,可在结节病病程中的任何时间出现。在此,我们报告2例已知患有结节病的患者,他们在没有已知原发性心脏病因的情况下出现了心脏异常。在我们的报告中,我们希望提请注意在任何系统性结节病病例中,尤其是在年轻患者中,考虑心脏受累的重要性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b504/4607964/f45837475939/PAMJ-21-243-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b504/4607964/facd3a835ce8/PAMJ-21-243-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b504/4607964/e48b022f1637/PAMJ-21-243-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b504/4607964/f45837475939/PAMJ-21-243-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b504/4607964/facd3a835ce8/PAMJ-21-243-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b504/4607964/e48b022f1637/PAMJ-21-243-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b504/4607964/f45837475939/PAMJ-21-243-g003.jpg

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